LEFT VENTRICULAR NON-COMPACTION IN DUCHENNE MUSCULAR DYSTROPHY
نویسندگان
چکیده
منابع مشابه
Left ventricular noncompaction in Duchenne muscular dystrophy
BACKGROUND Left ventricular noncompaction (LVNC) describes deep trabeculations in the left ventricular (LV) endocardium and a thinned epicardium. LVNC is seen both as a primary cardiomyopathy and as a secondary finding in other syndromes affecting the myocardium such as neuromuscular disorders. The objective of this study is to define the prevalence of LVNC in the Duchenne Muscular Dystrophy (D...
متن کاملLeft ventricular T2 distribution in Duchenne Muscular Dystrophy
BACKGROUND Although previous studies have helped define the natural history of Duchenne muscular dystrophy (DMD)-associated cardiomyopathy, the myocardial pathobiology associated with functional impairment in DMD is not yet known.The objective of this study was to assess the distribution of transverse relaxation time (T2) in the left ventricle (LV) of DMD patients, and to determine the associat...
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Duchenne muscular dystrophy (BMD) is an inherited X-link disease. The incidence of this muscle-wasting disease is 1:5000 male live births. Mutation in the gene coding for dystrophin is the main cause of BMD. Most cases of this disease succumb to respiratory and cardiac failure in 3rd to 4th decades. The slow progression of BMD and recent achievement of gene therapies make it as an appropriate c...
متن کاملLeft Ventricular Non-Compaction
OBJECTIVES We aimed to test the diagnostic accuracy of cardiovascular magnetic resonance (CMR) imaging in distinguishing pathological left ventricular non-compaction (LVNC) from lesser degrees of trabecular layering seen in healthy volunteers and, in those with cardiomyopathies and concentric left ventricular hypertrophy, potential differential diagnoses. We hypothesized that pathological trabe...
متن کاملLeft ventricular non-compaction.
To cite: Steger CM. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2013203430 DESCRIPTION In April 2011, a 13-month-old girl presented with dyspnoea, tachycardia and weight loss. Echocardiographic examination revealed a left ventricular non-compaction (LVNC), or spongy myocardium characterised by spongiform appearance of the left ventricle with deep recesses, a d...
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ژورنال
عنوان ژورنال: Journal of the American College of Cardiology
سال: 2012
ISSN: 0735-1097
DOI: 10.1016/s0735-1097(12)60822-5